Behcet's disease is a multisystemic disorder characterized by vasculitis. The clinical triad of relapsing uveitis with recurrent oral and genital ulceration was descibed by Hulusi Behcet, a Turkish dermatologist, in 1937. It's etiology remains
unknown.
Later, it was realized that there may be some other systemic manifestation of the disease at the time of diagnosis, including vascular lesions, central nervous system involvement, arthritis, pulmonary and gastrointestinal involvement. Behcet's
disease
may also begin with the manifestation of vascular involvement instead of the classical triad of symptoms. Behcet's disease is of interest to not only dermatologists and ophthalmologists but also to physicians of virtually every other specialty
because
it is a systemic disease that spares no organ in the body. Although vascular lesions are not listed among the criteria for diagnosis of Behcet's disease, up to 25~35% of patients develop vascular complications and probably an even greater
proportion of
patient may have small vessel vasculitis as the pathological basis of systemic manifestation. Here, we report 4 cases of Behcet disease, involuing abdominal aorta and its main branches with review of literature.
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